English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘enfermedad de Degos’. Meanings of “enfermedad de degos” in English Spanish Dictionary: 1 result(s) Meanings of “enfermedad de degos” with other terms in English Spanish. Me llamo Loli tengo 37 años y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo.
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Summary Epidemiology Less than cases have been described in the literature. Read this article in English. Systemic manifestations are progressive and may lead to serious complications: More developed lesions can imitate lichen sclerosus see this term. Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
Orphanet: Enfermedad de Degos
Print Send to a friend Export reference Mendeley Statistics. MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities.
CiteScore measures average citations received per enfermeda published. May Pages ee22 Pages Are you a health professional able to prescribe or dispense drugs? As all patients may potentially develop the systemic, life-threatening variant, an annual follow-up is mandatory. A clinical inspection of the skin should be combined with additional examinations including brain magnetic resonance tomography, gastroscopy, colonoscopy, X-ray of the chest and abdominal ultrasound, in order to assess the long-term prognosis.
Genetic counseling A genetic predisposition with an autosomal dominant trait has been suggested.
In early stages, histology of lesions may reveal a superficial and deep perivascular lymphocytic infiltration with distinct mucin deposition.
Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions. Later a wedge-shaped connective tissue necrosis in the deep dermis, due to a thrombotic occlusion of the small arteries and sparse lymphocytes, occurs. The histology of early lesions resembles cutaneous lupus erythematosus see this term.
SRJ is a prestige metric based on the idea that not all citations are the same. The documents contained in this web site are enfrrmedad for information purposes only. Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted.
Health care resources detos this disease Expert centres 69 Diagnostic tests 0 Patient organisations 21 Orphan drug s 0. This item has received. Show degoa Show less.
Over several days, the center of the lesions sinks and develops a characteristic morphology: Prognosis Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions. If you are a member of the AEDV: This condition is chronic and lesions persist over years, often throughout life.
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enfermedad de degos
Hypotheses implicating vasculitis, coagulopathy or a primary dysfunction of endothelial cells have been proposed. In the year has been indexed in the Medlinedatabase, and enefrmedad become a vehicle for expressing the most current Spanish medicine and modern.
It may more rarely manifest as pericarditis or in other organs such as the lungs, presenting as pleuritis. Many patients have been reported to have defects in blood coagulation.
enfermedad de Degos – English Translation – Word Magic Spanish-English Dictionary
Disease definition Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Only comments written in English can be processed.
Additional information Further information on this disease Classification s 3 Gene s 0 Clinical signs and symptoms Publications in PubMed Other degoe s 7. No effective treatment for the systemic manifestations has been established, however, subcutaneous treprostinil has been tested successfully in one case with intestinal and CNS manifestations. Face, scalp, palms of hands encermedad soles of feet are rarely involved. Subscriber If enfermedadd already have your login data, please click here.
Continuing navigation will be considered as acceptance of this use. Differential diagnosis The histology of early lesions resembles cutaneous lupus erythematosus see this term. From Monday to Friday from 9 a. Diagnostic methods Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic. More developed lesions show prominent changes in the dermoepidermal junction, with atrophy of the epidermis degoe an area of sclerosis in the papillary dermis.
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Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic. Go to the members area of the website of the AEDV, https: Ebfermedad article Next article. SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact.
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Summary and related texts. Other search option s Alphabetical list. Systemic lesions may affect the gastrointestinal tract and the central nervous system CNS and are potentially lethal. All articles are subjected to a rigorous process of revision in pairs, and careful editing for literary and xe style.